Budd-Chiari Syndrome
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Overview
Budd-Chiari Syndrome (BCS) is a rare condition caused by the obstruction of the veins that drain blood from the liver (hepatic veins). This blockage leads to impaired blood flow, causing liver congestion, swelling, and damage. If untreated, Budd-Chiari Syndrome can progress to liver failure and serious complications.
What Causes Budd-Chiari Syndrome?
Budd-Chiari Syndrome usually results from blood clots blocking the hepatic veins. Causes and risk factors include:
- Blood clotting disorders (thrombophilia)
- Myeloproliferative disorders (blood cell diseases)
- Cancer
- Infections
- Trauma or injury to the liver veins
- Certain medications
- Pregnancy or use of oral contraceptives
Who is at Risk for Budd-Chiari Syndrome?
- Individuals with conditions that increase blood clot risk.
- Patients with blood disorders like polycythemia vera or essential thrombocythemia.
- Women who are pregnant or taking hormonal contraceptives.
- People with cancer or inflammatory diseases.
- Patients with prior liver diseases.
What Are the Symptoms of Budd-Chiari Syndrome?
Symptoms can develop suddenly (acute) or gradually (chronic) and may include:
- Abdominal pain, especially in the upper right side
- Abdominal swelling due to fluid buildup (ascites)
- Enlarged liver (hepatomegaly)
- Jaundice (yellowing of skin and eyes)
- Fatigue and weakness
- Enlarged spleen
- Varices and gastrointestinal bleeding in advanced cases
How is Budd-Chiari Syndrome Diagnosed?
Diagnosis involves:
To check liver function and clotting status.
To assess blood flow in the hepatic veins.
To visualize the liver, veins, and any obstructions.
An imaging test where dye is injected to visualize veins.
How is Budd-Chiari Syndrome Treated?
Treatment depends on severity and cause:
- Medications: Blood thinners (anticoagulants) to prevent clotting.
- Procedures to restore blood flow: Angioplasty or stenting to open blocked veins.
- Shunt surgery: To bypass obstructed veins and relieve pressure.
- Liver transplantation: For severe liver damage or liver failure not responsive to other treatments.
When is Liver Transplantation Needed?
Liver transplantation is considered when Budd-Chiari Syndrome causes irreversible liver failure or when other treatments fail to control symptoms and complications. Transplant can restore liver function and improve survival.
How Can Liver Transplantation Portal Help You?
At Liver Transplantation Portal, we connect patients with Budd-Chiari Syndrome to expert hepatologists and transplant centers. Our platform provides personalized support from diagnosis to treatment and transplantation, ensuring access to the best care tailored to your needs.
Why Choose Liver Transplantation Portal?
We are dedicated to guiding patients with complex liver diseases like Budd-Chiari Syndrome. With access to leading specialists and transplant services, Liver Transplantation Portal ensures you receive compassionate, expert-led care throughout your liver health journey.
Contact us today to learn more about Budd-Chiari Syndrome and how we can assist you.